|Names||Criteria Used in Diagnosis/Source||When Is Diagnosis Established?|
|Takayasu arteritis (71)||Age of onset <40 y Intermittent claudication Diminished brachial artery pulse Subclavian artery or aortic bruit Systolic BP variation of >10 mm Hg between arms Aortographic evidence of aorta or aortic branch stenosis||≥3 criteria are present (sensitivity 90.5%; specificity 97.8%)|
|Giant cell arteritis (72)||Age >50 y Recent-onset localized headache Temporary artery tenderness or pulse attenuation Elevated erythrocyte sedimentation >50 mm/h Arterial biopsy shows necrotizing vasculitis||≥3 criteria are present (sensitivity >90%; specificity >90%)|
|Behçet disease (73)||Oral ulceration Recurrent genital ulceration Uveitis or retinal vasculits Skin lesions—erythema nodosum, pseudo-folliculitis, or pathergy||Oral ulceration plus 2 of the other 3 criteria|
|Ankylosing spondylitis (74)||Onset of pain <40 y Back pain for >3 months Morning stiffness Subtle symptom onset Improvement with exercise||4 of the diagnostic criteria are present|
BP indicates blood pressure.