Author + information
- Received April 28, 2009
- Revision received September 8, 2009
- Accepted September 14, 2009
- Published online August 10, 2010.
- Brijesh Patel, MD*,
- Yuliya Kats, MD*,
- Muhamed Saric, MD, PhD*,
- Pierre Maldjian, MD† and
- Marc Klapholz, MD*
A 49-year-old woman with exertional chest pain and a systolic murmur at the right upper sternal border radiating to both carotids had a hypercontractile left ventricle (LV) and a 77 mm Hg peak pressure gradient between the LV and the ascending aorta on transthoracic echocardiography (A). Transesophageal echocardiography revealed a membrane-like intimal thickening (B)with flow acceleration at the sinotubular junction (C, Online Video 1) and no anomalies of LV outflow tract or the aortic valve. Computed tomography demonstrated hourglass-shaped aortic root with 1-cm diameter at the stenosis (D, Online Video 2). Final diagnosis was supravalvular aortic stenosis. Hyperdynamic LV likely contributed to pressure gradient. The patient declined surgery.
- Received April 28, 2009.
- Revision received September 8, 2009.
- Accepted September 14, 2009.
- American College of Cardiology Foundation