Author + information
- Received July 13, 2010
- Accepted July 22, 2010
- Published online April 12, 2011.
A 19-month-old female presented with a new, asymptomatic, grade IV/VI systolic ejection murmur at the left upper sternal border. Transesophageal echocardiogram revealed a 19-mm ovoid mass occupying the main pulmonary artery (MPA) distal to the pulmonary valve (PV) (A and B). By echocardiogram, the mass was felt to originate from the MPA posterior wall. However, cardiovascular magnetic resonance demonstrated the mass originated within the right interventricular septum, involving the right ventricular outflow tract, PV, and MPA (Online Video 1). The mass appeared isointense on T1-weighted echo planar imaging (Online Video 2) and double inversion-recovery imaging (C). On T2-weighted imaging with fat suppression, the mass appeared hyperintense (D). Perfusion imaging did not demonstrate significant perfusion of the mass (Online Video 3). Post-gadolinium T1-weighted echo planar imaging revealed a hyperintense rim surrounding a hypointense core (E). Successful surgical resection of the mass required excision of PV leaflets, which were successfully reconstructed with CorMatrix (CorMatrix, Alpharetta, Georgia) (F). Histopathology confirmed the diagnosis of inflammatory myofibroblastic tumor (G).
- Received July 13, 2010.
- Accepted July 22, 2010.
- American College of Cardiology Foundation