Author + information
- Received December 5, 2013
- Accepted December 23, 2013
- Published online May 6, 2014.
- Rajiv Bharat Kharwar, MD,
- Sudhanshu Kumar Dwivedi, MD, DM,
- Sharad Chandra, MD, DM and
- Ram Kirti Saran, MD, DM
An 11-year-old cyanotic boy presented to our department with worsening effort intolerance. Two-dimensional transthoracic echocardiography with color Doppler (A to D, Online Video 1) showed a common truncus originating over a large nonrestrictive ventricular septal defect (VSD) with the main pulmonary artery (MPA) trunk originating from the posterior aspect of the truncus (Van Praagh classification type I). There was moderate regurgitation of the truncal valve. Three-dimensional transthoracic echocardiography (E and F, Online Videos 2 and 3) further delineated the anatomy, and the diagnosis of persistent truncus arteriosus was confirmed on multidetector computed tomography with 3-dimensional volume rendering (G to J).
Persistent truncus arteriosus is a rare congenital heart defect, and 90% of patients with this defect die before 1 year of age. Survival beyond the first decade is even rarer. LPA = left pulmonary artery; LV = left ventricle; RPA = right pulmonary artery; RV = right ventricle.
- Received December 5, 2013.
- Accepted December 23, 2013.
- American College of Cardiology Foundation