Author + information
- Fabiola Sozzia,b,
- Nicolas Huguesa,b,
- Laura Iacuzioa,b,
- Francois Bourlona,b,
- Filippo Civaiaa,b,
- Gilles Dreyfusa,b and
- Vincent Dora,b
Background: Congenital coronary artery fistulas (CAF) with significant clinical impact are extremely rare vascular anomalies. Little data are available.
Aim: To determine the outcome of percutaneous closure of large hemodynamically significant CAF in young patients.
Methods: We retrospectively analysed 11 patients (median age at intervention 21 years, 3 females) affected by relevant congenital CAF, diagnosed by echocardiogram and cardiac catheterization. All patients underwent percutaneous closure and were followed for a mean period of 3 years.
Results: The clinical presentation of CAF was characterized by symptoms in 7/11 cases. In the other 4 cases CAF was incidentally diagnosed by echocardiogram. In most cases the fistulas were originating from the left coronary artery (LCA) [7/11]. The right heart was the most common site of drainage (8/11). Multiple fistulas were found in 3 patients. No-one had other congenital disorders associated. All patients were treated with percutaneous transcatheter embolization. During follow-up, no patient died. In 1 case a retrograde thrombosis of the fistula with acute myocardial infarction occurred after 1 month and was treated with thrombectomy and coronary bypass. No other major adverse cardiac events were recorded.
Conclusions: Percutaneous closure of significant coronary fistulas is associated with low event-rate and excellent prognosis.
Poster Hall, Hall C
Friday, March 17, 2017, 3:45 p.m.-4:30 p.m.
Session Title: Innovations in Pediatric Catheterization and EP: Mending, Fixing and Predicting
Abstract Category: 11. Congenital Heart Disease: Therapy
Presentation Number: 1144-021
- 2017 American College of Cardiology Foundation