Author + information
- James S. Tweddella,b,
- Shagun Sachdevaa,b,
- Ronald Woodsa,b,
- Michael Mitchella,b,
- Joseph Cavaa,b,
- Nancy Ghanayema,b,
- Peter Bartza,b and
- Peter Frommelta,b
Background: Congenitally corrected transposition of the great arteries (CCTGA) is a rare cardiac malformation resulting from abnormal looping of the embryonic cardiac tube that results in atrioventricular and ventriculoarterial discordance. Surgical options include a physiologic repair (PR) or anatomic repair (AR). PR involves correction of the associated cardiac defects, leaving the morphologic right ventricle (RV) as the systemic ventricle and is associated with poor late survival. AR consists of an atrial switch operation combined with an arterial switch or Rastelli procedure and returns the morphologic left ventricle to the systemic position. Our aim was to review our outcomes with AR.
Methods: Retrospective analysis of 15 patients who underwent AR for CCTGA from 2001-2015.
Results: Two patients were lost to follow-up. Median duration of follow up was 4.5 years (0.05 −14 yrs). There have been no early or late deaths. No patients had heart failure symptoms. 12/13 patients (92%) had normal biventricular systolic function and 1 patient (7.6%) had mildly diminished left ventricular function.
Conclusions: AR repair can be applied to patients with CCTGA with excellent survival and functional status but reoperations are common. Bidirectional Glenn shunt is indicated for morphologic RV hypoplasia but should not be part of routine AR.
Poster Hall, Hall C
Sunday, March 19, 2017, 9:45 a.m.-10:30 a.m.
Session Title: Congenital Heart Disease Surgery: Updates and Innovations
Abstract Category: 11. Congenital Heart Disease: Therapy
Presentation Number: 1272-022
- 2017 American College of Cardiology Foundation