Table 1

Demographics

Alive
(n = 31)
Deceased (n = 11)p ValueTotal Cohort (N = 42)
Median age at PLE diagnosis, yrs14 (4.7–57)22 (12–39)0.0117 (4.7–57)
Median age at Fontan operation, yrs8 (2–38)11.9 (2–37)NS8.3 (2–38)
Median time: Fontan operation to PLE, yrs6.5 (1–27)10.4 (1–20)NS7.8 (1–27)
Male16 (52)7 (64)NS23 (55)
Type of initial Fontan operationNS
 Atriopulmonary connections19 (61)9 (81)28 (67)
 Lateral tunnel or intra-atrial conduit4 (13)2 (19)6 (14)
 Extracardiac conduit8 (26)08 (19)
Predominant ventricular morphologyNS
 Left19 (61)8 (73)27 (64)
 Right12 (39)3 (27)15 (36)

Values are mean (range) or n (%).

NS = not significant; PLE = protein-losing enteropathy.